Focal myoclonus‐dystonia of the leg secondary to a lesion of the posterolateral putamen: Clinical and neurophysiological features
Identifieur interne : 004083 ( Main/Exploration ); précédent : 004082; suivant : 004084Focal myoclonus‐dystonia of the leg secondary to a lesion of the posterolateral putamen: Clinical and neurophysiological features
Auteurs : Neil Mahant [Australie] ; Dennis J. Cordato [Australie] ; Victor S. C. Fung [Australie]Source :
- Movement Disorders [ 0885-3185 ] ; 2003-04.
Descripteurs français
- Pascal (Inist)
- Wicri :
- topic : Homme.
English descriptors
- KwdEn :
- Adult, Atrophy, Basal Ganglia Diseases (diagnosis), Basal Ganglia Diseases (physiopathology), Case study, Dominance, Cerebral (physiology), Dystonia, Dystonia (diagnosis), Dystonia (physiopathology), Electromyography, Etiology, Female, Focal lesion, Gliosis, Gliosis (diagnosis), Gliosis (pathology), Human, Humans, Leg (innervation), Magnetic Resonance Imaging, Muscle, Skeletal (innervation), Myoclonus, Myoclonus (diagnosis), Myoclonus (physiopathology), Neurologic Examination, Nuclear magnetic resonance imaging, Putamen, Putamen (pathology), Putamen (physiopathology), Reflex, Abnormal (physiology), Video recording, basal ganglia, dystonia, myoclonus, neurophysiology, putamen, somatotopy.
- MESH :
- diagnosis : Basal Ganglia Diseases, Dystonia, Gliosis, Myoclonus.
- innervation : Leg, Muscle, Skeletal.
- pathology : Gliosis, Putamen.
- physiology : Dominance, Cerebral, Reflex, Abnormal.
- physiopathology : Basal Ganglia Diseases, Dystonia, Myoclonus, Putamen.
- Adult, Atrophy, Electromyography, Female, Humans, Magnetic Resonance Imaging, Neurologic Examination.
Abstract
We report on a patient with spontaneous and stimulus‐sensitive myoclonic jerks and dystonia of the right leg that had been present since infancy. Magnetic resonance imaging showed a linear area of gliosis confined to the left posterolateral putamen. This is the first report of focal myoclonus‐dystonia of the lower limb secondary to a putaminal lesion. © 2003 Movement Disorder Society
Url:
DOI: 10.1002/mds.10382
Affiliations:
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Le document en format XML
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<term>Dystonia (physiopathology)</term>
<term>Electromyography</term>
<term>Etiology</term>
<term>Female</term>
<term>Focal lesion</term>
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<term>Magnetic Resonance Imaging</term>
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<term>Putamen (pathology)</term>
<term>Putamen (physiopathology)</term>
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<term>Video recording</term>
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<term>Gliosis</term>
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<front><div type="abstract" xml:lang="en">We report on a patient with spontaneous and stimulus‐sensitive myoclonic jerks and dystonia of the right leg that had been present since infancy. Magnetic resonance imaging showed a linear area of gliosis confined to the left posterolateral putamen. This is the first report of focal myoclonus‐dystonia of the lower limb secondary to a putaminal lesion. © 2003 Movement Disorder Society</div>
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